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A rare case of skin blistering and esophageal stenosis in the course of epidermolysis bullosa - case report and literature review

Overview of attention for article published in BMC Gastroenterology, April 2018
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About this Attention Score

  • Above-average Attention Score compared to outputs of the same age (56th percentile)

Mentioned by

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3 tweeters

Citations

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2 Dimensions

Readers on

mendeley
10 Mendeley
Title
A rare case of skin blistering and esophageal stenosis in the course of epidermolysis bullosa - case report and literature review
Published in
BMC Gastroenterology, April 2018
DOI 10.1186/s12876-018-0771-5
Pubmed ID
Authors

Agata Michalak, Halina Cichoż-Lach, Beata Prozorow-Król, Leszek Buk, Monika Dzida

Abstract

Epidermolysis bullosa (EB) constitutes a heterogenous group of rare multisystem genetically transmitted disorders comprising several blistering muco-cutaneous diseases with a monogenic basis and either autosomal dominant or autosomal recessive mode of inheritance. EB manifestation is not only limited to the skin. Systemic signs might involve the nose, ear, eye, genitourinary tract and upper gastrointestinal tract. The presence of particular symptoms is directly determined by a type of altered skin protein. Gastrointestinal manifestation of EB is most commonly reflected by esophageal stenosis due to recurrent esophageal blistering, followed by consequent scarring. Here we present a case of a man with dystrophic EB and dysphagia, skin blistering, joints contractures and missing nails. To our knowledge, the presented man is the oldest one diagnosed with EB living in Poland. Management of an esophageal stricture in such circumstances is based on endoscopic dilatation. However, in most severe cases, placement of a gastrostomy tube is required. Despite great advances in medicine, a targeted therapy in the course of EB has not been established yet.

Twitter Demographics

The data shown below were collected from the profiles of 3 tweeters who shared this research output. Click here to find out more about how the information was compiled.

Mendeley readers

The data shown below were compiled from readership statistics for 10 Mendeley readers of this research output. Click here to see the associated Mendeley record.

Geographical breakdown

Country Count As %
Unknown 10 100%

Demographic breakdown

Readers by professional status Count As %
Unspecified 4 40%
Student > Doctoral Student 2 20%
Student > Ph. D. Student 1 10%
Student > Master 1 10%
Other 1 10%
Other 1 10%
Readers by discipline Count As %
Unspecified 4 40%
Medicine and Dentistry 4 40%
Psychology 1 10%
Biochemistry, Genetics and Molecular Biology 1 10%

Attention Score in Context

This research output has an Altmetric Attention Score of 3. This is our high-level measure of the quality and quantity of online attention that it has received. This Attention Score, as well as the ranking and number of research outputs shown below, was calculated when the research output was last mentioned on 08 May 2018.
All research outputs
#6,786,138
of 12,907,794 outputs
Outputs from BMC Gastroenterology
#269
of 838 outputs
Outputs of similar age
#115,411
of 270,332 outputs
Outputs of similar age from BMC Gastroenterology
#1
of 1 outputs
Altmetric has tracked 12,907,794 research outputs across all sources so far. This one is in the 46th percentile – i.e., 46% of other outputs scored the same or lower than it.
So far Altmetric has tracked 838 research outputs from this source. They receive a mean Attention Score of 4.6. This one has gotten more attention than average, scoring higher than 66% of its peers.
Older research outputs will score higher simply because they've had more time to accumulate mentions. To account for age we can compare this Altmetric Attention Score to the 270,332 tracked outputs that were published within six weeks on either side of this one in any source. This one has gotten more attention than average, scoring higher than 56% of its contemporaries.
We're also able to compare this research output to 1 others from the same source and published within six weeks on either side of this one. This one has scored higher than all of them